Born seemingly healthy and sent home with their families, 2 decades ago infants with SCID were typically not diagnosed with their fatal disease until they developed recurrent and severe infections months later. Hematopoietic stem cell (HSC) transplantation (HSCT), also known as bone marrow transplantation, was established as an effective treatment for SCID by the 1980s. However, without a family history or an astute clinician familiar with this rare disease, infants frequently died prior to diagnosis and transplantation. Children who received a diagnosis often had malnutrition and critical illness at the time of transplantation, leading to morbidity and mortality. Dr. Rebecca H. Buckley and colleagues hypothesized that treatment of these babies very early in life, prior to developing infections, would improve outcomes. In this Pillars of Immunology article, the study of infants who received HSCT in the first month of life compared with those treated later paved the way for early...
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1 February 2023
Research Article|
February 01 2023
Early Is the Key for Treatment of Severe Combined Immunodeficiency
Megan A. Cooper
Department of Pediatrics, Division of Rheumatology & Immunology, Washington University School of Medicine in St. Louis, St. Louis, MO; and Department of Pathology & Immunology, Washington University School of Medicine in St. Louis, St. Louis, MO
Address correspondence and reprint requests to Dr. Megan A. Cooper, Washington University School of Medicine in St. Louis, 660 South Euclid Avenue, Box 8208, St. Louis, MO 63110. E-mail address: cooper_m@wustl.edu
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Address correspondence and reprint requests to Dr. Megan A. Cooper, Washington University School of Medicine in St. Louis, 660 South Euclid Avenue, Box 8208, St. Louis, MO 63110. E-mail address: cooper_m@wustl.edu
Online ISSN: 1550-6606
Print ISSN: 0022-1767
Copyright © 2023 by The American Association of Immunologists, Inc.
2023
Copyright © 2023 by The American Association of Immunologists, Inc.
J Immunol (2023) 210 (3): 219–220.
Citation
Megan A. Cooper; Early Is the Key for Treatment of Severe Combined Immunodeficiency. J Immunol 1 February 2023; 210 (3): 219–220. https://doi.org/10.4049/jimmunol.2200840
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